Name: Name:1-Propanaminium, 3-carboxy-2-(4-carboxy-1-oxobutoxy)-N,N,N-trimethyl-, inner salt, (2R)-
Brand: AABLOCKS
SKU: AA0007X2
Rating: 90 (10 reviews)

Catalog No.:AA0007X2

102636-82-8 | 1-Propanaminium, 3-carboxy-2-(4-carboxy-1-oxobutoxy)-N,N,N-trimethyl-, inner salt, (2R)-

Pack Size

Purity

Availability

Price(USD)

Quantity

5mg

98%

2 weeks

$190.00 $133.00

- +

Technical Information
Properties
Literature
Request for Quotation
Q & A

Technical Information
Properties
Literature

Technical Information

Catalog Number:

AA0007X2

Chemical Name:

1-Propanaminium, 3-carboxy-2-(4-carboxy-1-oxobutoxy)-N,N,N-trimethyl-, inner salt, (2R)-

CAS Number:

102636-82-8

Molecular Formula:

C12H21NO6

Molecular Weight:

275.2982

MDL Number:

MFCD16036250

IUPAC Name:

(3R)-3-(4-carboxybutanoyloxy)-4-(trimethylazaniumyl)butanoate

InChI:

InChI=1S/C12H21NO6/c1-13(2,3)8-9(7-11(16)17)19-12(18)6-4-5-10(14)15/h9H,4-8H2,1-3H3,(H-,14,15,16,17)/t9-/m1/s1

InChI Key:

NXJAXUYOQLTISD-SECBINFHSA-N

SMILES:

O=C(O[[email protected]@H](C[N+](C)(C)C)CC(=O)O)CCCC(=O)[O-]

Properties

Computed Properties

Complexity:

328

Compound Is Canonicalized:

Yes

Covalently-Bonded Unit Count:

Defined Atom Stereocenter Count:

Defined Bond Stereocenter Count:

Exact Mass:

275.137g/mol

Formal Charge:

Heavy Atom Count:

Hydrogen Bond Acceptor Count:

Hydrogen Bond Donor Count:

Isotope Atom Count:

Molecular Weight:

275.301g/mol

Monoisotopic Mass:

275.137g/mol

Rotatable Bond Count:

Topological Polar Surface Area:

104A^2

Undefined Atom Stereocenter Count:

Undefined Bond Stereocenter Count:

XLogP3:

0.2

Synonyms

glutarylcarnitine

Glutarylcarnitine

(3R)-3-[(4-carboxybutanoyl)oxy]-4-(trimethylammonio)butanoate

(3R)-3-[(4-Carboxybutanoyl)oxy]-4-(trimethylazaniumyl)butanoate

(2R)-3-Carboxy-2-(4-carboxy-1-oxobutoxy)-N,N,N-trimethyl-1-propanaminium Inner Salt

L-Glutaryl Carnitine See G597605

102636-82-8

glutaroyl carnitine

glutaryl-L-carnitine

L-Glutaryl Carnitine

O-glutaroyl-L-carnitine

CHEBI:82952

DTXSID40747861

J-000747

Literature

Title: An improved LC-MS/MS method for the detection of classic and low excretor glutaric acidemia type 1.

Journal: Journal of inherited metabolic disease 20120501

Title: Therapeutic modulation of cerebral L-lysine metabolism in a mouse model for glutaric aciduria type I.

Journal: Brain : a journal of neurology 20110101

Title: Comparison of amino acids and acylcarnitines assay methods used in newborn screening assays by tandem mass spectrometry.

Journal: Clinica chimica acta; international journal of clinical chemistry 20100502

Title: False-positive newborn screening mimicking glutaric aciduria type I in infants with renal insufficiency.

Journal: Journal of inherited metabolic disease 20091201

Title: Enzymatic evaluation of glutaric acidemia type 1 by an in vitro probe assay of acylcarnitine profiling using fibroblasts and electrospray ionization/tandem mass spectrometry (MS/MS).

Journal: Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20090901

Title: Maternal glutaric acidemia, type I identified by newborn screening.

Journal: Molecular genetics and metabolism 20080501

Title: Neonatal screening for glutaric aciduria type I: strategies to proceed.

Journal: Journal of inherited metabolic disease 20060101

Title: Glutaryl-CoA dehydrogenase deficiency and newborn screening: retrospective analysis of a low excretor provides further evidence that some cases may be missed.

Journal: Molecular genetics and metabolism 20051101

Title: The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I.

Journal: Molecular genetics and metabolism 20050201

Title: Genetic and biochemical study in a patient with glutaric acidemia type I.

Journal: Journal of the Formosan Medical Association = Taiwan yi zhi 20040701

Title: Pseudo-glutarylcarnitinaemia in medium-chain acyl-CoA dehydrogenase deficiency detected by tandem mass spectrometry newborn screening.

Journal: Journal of inherited metabolic disease 20040101

Title: Stability of malonylcarnitine and glutarylcarnitine in stored blood spots.

Journal: Journal of inherited metabolic disease 20040101

Title: Glutaryl-CoA dehydrogenase deficiency: region-specific analysis of organic acids and acylcarnitines in post mortem brain predicts vulnerability of the putamen.

Journal: Neuropediatrics 20030601

Quotation Request

Q & A