[1]ZhurnalObshcheiKhimii,1955,vol.25,p.1218,1221;engl.Ausg.S.1165
[1]JournalofBiologicalChemistry,1949,vol.180,p.971-974
[2]JournalofBiologicalChemistry,1949,vol.180,p.971-974
[1]JustusLiebigsAnnalenderChemie,1925,vol.442,p.144,147 JustusLiebigsAnnalenderChemie,1926,vol.447,p.259
[1]CanadianJournalofChemistry,1954,vol.32,p.1012,1014
Title: Urinary metabolic phenotyping the slc26a6 (chloride-oxalate exchanger) null mouse model.
Journal: Journal of proteome research 20120907
Title: A simple screening method using ion chromatography for the diagnosis of cerebral creatine deficiency syndromes.
Journal: Amino acids 20120801
Title: Creatine and guanidinoacetate transport at blood-brain and blood-cerebrospinal fluid barriers.
Journal: Journal of inherited metabolic disease 20120701
Title: Developmental progress and creatine restoration upon long-term creatine supplementation of a patient with arginine:glycine amidinotransferase deficiency.
Journal: Molecular genetics and metabolism 20120501
Title: Gas chromatographic determination of guanidino compounds in uremic patients using glyoxal as derivatizing reagent.
Journal: Journal of chromatographic science 20120501
Title: Expression and function of arginine-producing and consuming-enzymes in the kidney.
Journal: Amino acids 20120401
Title: Supplementation of guanidinoacetic acid to broiler diets: effects on performance, carcass characteristics, meat quality, and energy metabolism.
Journal: Poultry science 20120201
Title: Long-term follow-up and treatment in nine boys with X-linked creatine transporter defect.
Journal: Journal of inherited metabolic disease 20120101
Title: Evaluation of two year treatment outcome and limited impact of arginine restriction in a patient with GAMT deficiency.
Journal: Molecular genetics and metabolism 20120101
Title: Enumerating metabolic pathways for the production of heterologous target chemicals in chassis organisms.
Journal: BMC systems biology 20120101
Title: Creatine protects against excitoxicity in an in vitro model of neurodegeneration.
Journal: PloS one 20120101
Title: γ-Aminobutyric acid transporter 2 mediates the hepatic uptake of guanidinoacetate, the creatine biosynthetic precursor, in rats.
Journal: PloS one 20120101
Title: ArgR of Streptomyces coelicolor is a versatile regulator.
Journal: PloS one 20120101
Title: Proteomics analysis of differentially expressed proteins in chicken trachea and kidney after infection with the highly virulent and attenuated coronavirus infectious bronchitis virus in vivo.
Journal: Proteome science 20120101
Title: Nutritional manipulation of one-carbon metabolism: effects on arsenic methylation and toxicity.
Journal: Journal of toxicology 20120101
Title: The languages spoken in the water body (or the biological role of cyanobacterial toxins).
Journal: Frontiers in microbiology 20120101
Title: In vitro study of uptake and synthesis of creatine and its precursors by cerebellar granule cells and astrocytes suggests some hypotheses on the physiopathology of the inherited disorders of creatine metabolism.
Journal: BMC neuroscience 20120101
Title: Guanidinoacetate methyltransferase (GAMT) deficiency in two Tunisian siblings: clinical and biochemical features.
Journal: Clinical laboratory 20120101
Title: Simultaneous determination of creatine and guanidinoacetate in plasma by liquid chromatography-tandem mass spectrometry (LC-MS/MS).
Journal: Journal of pharmaceutical and biomedical analysis 20111205
Title: Identification of amino acid residues responsible for taurocyamine binding in mitochondrial taurocyamine kinase from Arenicola brasiliensis.
Journal: Biochimica et biophysica acta 20111001
Title: Creatine transporter defect diagnosed by proton NMR spectroscopy in males with intellectual disability.
Journal: American journal of medical genetics. Part A 20111001
Title: Creatinine, diet, micronutrients, and arsenic methylation in West Bengal, India.
Journal: Environmental health perspectives 20110901
Title: trans-Diaqua-bis-(dl-valinato-κN,O)nickel(II).
Journal: Acta crystallographica. Section E, Structure reports online 20110901
Title: Low homoarginine concentration is a novel risk factor for heart disease.
Journal: Heart (British Cardiac Society) 20110801
Title: Prediction of variability in CYP3A4 induction using a combined 1H NMR metabonomics and targeted UPLC-MS approach.
Journal: Journal of proteome research 20110603
Title: Creatine deficiency syndromes and the importance of creatine synthesis in the brain.
Journal: Amino acids 20110501
Title: Metabolomics reveals target and off-target toxicities of a model organophosphate pesticide to roach (Rutilus rutilus): implications for biomonitoring.
Journal: Environmental science & technology 20110415
Title: Assessing learning and memory in pigs.
Journal: Animal cognition 20110301
Title: Metabolic regulation by p53.
Journal: Journal of molecular medicine (Berlin, Germany) 20110301
Title: Disorders of creatine transport and metabolism.
Journal: American journal of medical genetics. Part C, Seminars in medical genetics 20110215
Title: 1H-MRS in spinal cord injury: acute and chronic metabolite alterations in rat brain and lumbar spinal cord.
Journal: The European journal of neuroscience 20110201
Title: Metabonomic investigation of single and multiple strain Trypanosoma brucei brucei infections.
Journal: The American journal of tropical medicine and hygiene 20110105
Title: Methylation cycle, arginine-creatine pathway and asymmetric dimethylarginine in paediatric renal transplant.
Journal: Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20110101
Title: Identification of urinary biomarkers of colon inflammation in IL10-/- mice using Short-Column LCMS metabolomics.
Journal: Journal of biomedicine & biotechnology 20110101
Title: Transport characteristics of guanidino compounds at the blood-brain barrier and blood-cerebrospinal fluid barrier: relevance to neural disorders.
Journal: Fluids and barriers of the CNS 20110101
Title: Should metabolic diseases be systematically screened in nonsyndromic autism spectrum disorders?
Journal: PloS one 20110101
Title: Linking hydrothermal geochemistry to organismal physiology: physiological versatility in Riftia pachyptila from sedimented and basalt-hosted vents.
Journal: PloS one 20110101
Title: Integrating transcriptomics and metabonomics to unravel modes-of-action of 2,3,7,8-tetrachlorodibenzo-p-dioxin (TCDD) in HepG2 cells.
Journal: BMC systems biology 20110101
Title: Stuck at the bench: Potential natural neuroprotective compounds for concussion.
Journal: Surgical neurology international 20110101
Title: A novel mutation in the HSD17B10 gene of a 10-year-old boy with refractory epilepsy, choreoathetosis and learning disability.
Journal: PloS one 20110101
Title: Methionine and serine synergistically suppress hyperhomocysteinemia induced by choline deficiency, but not by guanidinoacetic acid, in rats fed a low casein diet.
Journal: Bioscience, biotechnology, and biochemistry 20110101
Title: Ethylene glycol monomethyl ether-induced toxicity is mediated through the inhibition of flavoprotein dehydrogenase enzyme family.
Journal: Toxicological sciences : an official journal of the Society of Toxicology 20101201
Title: Phosphagen kinases of parasites: unexplored chemotherapeutic targets.
Journal: The Korean journal of parasitology 20101201
Title: An Update on GABAρ Receptors.
Journal: Current neuropharmacology 20101201
Title: GC/MS determination of guanidinoacetate and creatine in urine: A routine method for creatine deficiency syndrome diagnosis.
Journal: Clinical biochemistry 20101101
Title: Functional and immunocytochemical characterization of the creatine transporter in rat hippocampal neurons.
Journal: Journal of neurochemistry 20101101
Title: Is there a role for routinely screening children with autism spectrum disorder for creatine deficiency syndrome?
Journal: Autism research : official journal of the International Society for Autism Research 20101001
Title: Simultaneous determination of guanidinosuccinic acid and guanidinoacetic acid in urine using high performance liquid chromatography/tandem mass spectrometry.
Journal: Analytica chimica acta 20100916
Title: Creatine prevents the inhibition of energy metabolism and lipid peroxidation in rats subjected to GAA administration.
Journal: Metabolic brain disease 20100901
Title: Creatine transporter deficiency in two half-brothers.
Journal: American journal of medical genetics. Part A 20100801
Title: Metabolic changes reveal the development of schistosomiasis in mice.
Journal: PLoS neglected tropical diseases 20100801
Title: Structural basis for the mechanism and substrate specificity of glycocyamine kinase, a phosphagen kinase family member.
Journal: Biochemistry 20100309
Title: Creatine and creatine deficiency syndromes: biochemical and clinical aspects.
Journal: Pediatric neurology 20100301
Title: Guanidinoacetate methyltransferase deficiency (GAMT).
Journal: Brain & development 20100201
Title: Dissociation of AGAT, GAMT and SLC6A8 in CNS: relevance to creatine deficiency syndromes.
Journal: Neurobiology of disease 20100201
Title: NMR-based metabolic profiling identifies biomarkers of liver regeneration following partial hepatectomy in the rat.
Journal: Journal of proteome research 20100101
Title: [(1)H] magnetic resonance spectroscopy of urine: diagnosis of a guanidinoacetate methyl transferase deficiency case.
Journal: Journal of child neurology 20100101
Title: Diagnosis of creatine metabolism disorders by determining creatine and guanidinoacetate in plasma and urine.
Journal: Methods in molecular biology (Clifton, N.J.) 20100101
Title: Guanidino compound levels in blood, cerebrospinal fluid, and post-mortem brain material of patients with argininemia.
Journal: Molecular genetics and metabolism 20100101
Title: Creatine metabolism and the urea cycle.
Journal: Molecular genetics and metabolism 20100101
Title: On the chemistry, toxicology and genetics of the cyanobacterial toxins, microcystin, nodularin, saxitoxin and cylindrospermopsin.
Journal: Marine drugs 20100101
Title: Adult Polyglucosan Body Disease (APBD): Anaplerotic diet therapy (Triheptanoin) and demonstration of defective methylation pathways.
Journal: Molecular genetics and metabolism 20100101
Title: l-arginine:glycine amidinotransferase (AGAT) deficiency: clinical presentation and response to treatment in two patients with a novel mutation.
Journal: Molecular genetics and metabolism 20100101
Title: Guanidino compounds as cause of cardiovascular damage in chronic kidney disease: an in vitro evaluation.
Journal: Blood purification 20100101
Title: Metabolomic investigations of American oysters using H-NMR spectroscopy.
Journal: Marine drugs 20100101
Title: Mitochondrial therapy for Parkinson's disease: neuroprotective pharmaconutrition may be disease-modifying.
Journal: Clinical pharmacology : advances and applications 20100101
Title: Simultaneous assay of isotopic enrichment and concentration of guanidinoacetate and creatine by gas chromatography-mass spectrometry.
Journal: Analytical biochemistry 20091201
Title: [Cerebral creatine deficiency: first Spanish patients harbouring mutations in GAMT gene].
Journal: Medicina clinica 20091121
Title: Guanidino acids act as rho1 GABA(C) receptor antagonists.
Journal: Neurochemical research 20091001
Title: The blood-brain barrier transport and cerebral distribution of guanidinoacetate in rats: involvement of creatine and taurine transporters.
Journal: Journal of neurochemistry 20091001
Title: The effect of L-arginine and creatine on vascular function and homocysteine metabolism.
Journal: Vascular medicine (London, England) 20090801
Title: Guanidinoacetate methyltransferase (GAMT) deficiency diagnosed by proton NMR spectroscopy of body fluids.
Journal: NMR in biomedicine 20090601
Title: Secondary creatine deficiency in ornithine delta-aminotransferase deficiency.
Journal: Molecular genetics and metabolism 20090601
Title: The role of Arg-96 in Danio rerio creatine kinase in substrate recognition and active center configuration.
Journal: International journal of biological macromolecules 20090601
Title: Advances in protein-amino acid nutrition of poultry.
Journal: Amino acids 20090501
Title: MRS is the test of choice for detecting and monitoring disorders of creatine metabolism.
Journal: Pediatric neurology 20090501
Title: Guanidinoacetate methyltransferase (GAMT) deficiency: late onset of movement disorder and preserved expressive language.
Journal: Developmental medicine and child neurology 20090501
Title: Folate, Cobalamin, Cysteine, Homocysteine, and Arsenic Metabolism among Children in Bangladesh.
Journal: Environmental health perspectives 20090501
Title: Low creatinine: the diagnostic clue for a treatable neurologic disorder.
Journal: Neurology 20090303
Title: Creatine synthesis: hepatic metabolism of guanidinoacetate and creatine in the rat in vitro and in vivo.
Journal: American journal of physiology. Endocrinology and metabolism 20090201
Title: FT-IR vibrational spectrum and DFT:B3LYP/6-31G and B3LYP/6-311G structure and vibrational analysis of glycinate-guanidoacetate nickel (II) complex: [Ni(Gly)(Gaa)].
Journal: Spectrochimica acta. Part A, Molecular and biomolecular spectroscopy 20090201
Title: Folate deficiency, hyperhomocysteinemia, low urinary creatinine, and hypomethylation of leukocyte DNA are risk factors for arsenic-induced skin lesions.
Journal: Environmental health perspectives 20090201
Title: Hypohomocysteinemic effect of cysteine is associated with increased plasma cysteine concentration in rats fed diets low in protein and methionine levels.
Journal: Journal of nutritional science and vitaminology 20090201
Title: Determination of creatine and guanidinoacetate by GC-MS: study of their stability in urine at different temperatures.
Journal: Clinical biochemistry 20090101
Title: Expanded clinical and molecular spectrum of guanidinoacetate methyltransferase (GAMT) deficiency.
Journal: Molecular genetics and metabolism 20090101
Title: Arginine, scurvy and Cartier's 'tree of life'.
Journal: Journal of ethnobiology and ethnomedicine 20090101
Title: Effect of betaine supplementation on power performance and fatigue.
Journal: Journal of the International Society of Sports Nutrition 20090101
Title: The orally active antihyperglycemic drug beta-guanidinopropionic acid is transported by the human proton-coupled amino acid transporter hPAT1.
Journal: Molecular pharmaceutics 20090101
Title: Predicting metabolic biomarkers of human inborn errors of metabolism.
Journal: Molecular systems biology 20090101
Title: Developmental changes in the expression of creatine synthesizing enzymes and creatine transporter in a precocial rodent, the spiny mouse.
Journal: BMC developmental biology 20090101
Title: Recent advances in the pathogenesis of syndromic autisms.
Journal: International journal of pediatrics 20090101
Title: Folate nutrition is related to neuropsychological functions in the elderly.
Journal: Nutrition research and practice 20090101
Title: Proteomic analysis of regenerating mouse liver following 50% partial hepatectomy.
Journal: Proteome science 20090101
Title: Enzymes of creatine biosynthesis, arginine and methionine metabolism in normal and malignant cells.
Journal: The FEBS journal 20081201
Title: High-casein diet suppresses guanidinoacetic acid-induced hyperhomocysteinemia and potentiates the hypohomocysteinemic effect of serine in rats.
Journal: Bioscience, biotechnology, and biochemistry 20081201
Title: Expression and possible role of creatine transporter in the brain and at the blood-cerebrospinal fluid barrier as a transporting protein of guanidinoacetate, an endogenous convulsant.
Journal: Journal of neurochemistry 20081101
Title: Simultaneous determination of guanidinoacetate, creatine and creatinine in urine and plasma by un-derivatized liquid chromatography-tandem mass spectrometry.
Journal: Annals of clinical biochemistry 20081101
Title: Inhibitory effect of fermented papaya preparation on hydroxyl radical generation from methylguanidine.
Journal: Journal of clinical biochemistry and nutrition 20081101
Title: Age related changes in brain metabolites observed by 1H MRS in APP/PS1 mice.
Journal: Neurobiology of aging 20080901
Title: Guanidinoacetate decreases antioxidant defenses and total protein sulfhydryl content in striatum of rats.
Journal: Neurochemical research 20080901
Title: Creatine uptake in mouse hearts with genetically altered creatine levels.
Journal: Journal of molecular and cellular cardiology 20080901
Title: The arginine-creatine pathway is disturbed in children and adolescents with renal transplants.
Journal: Pediatric research 20080801
Title: Reduced brain choline in homocystinuria due to remethylation defects.
Journal: Neurology 20080701
Title: Metabolic profiling of an Echinostoma caproni infection in the mouse for biomarker discovery.
Journal: PLoS neglected tropical diseases 20080701
Title: Hyperhomocysteinemia induced by guanidinoacetic acid is effectively suppressed by choline and betaine in rats.
Journal: Bioscience, biotechnology, and biochemistry 20080701
Title: Effects in vitro of guanidinoacetate on adenine nucleotide hydrolysis and acetylcholinesterase activity in tissues from adult rats.
Journal: Neurochemical research 20080601
Title: Guanidinoacetate administration increases acetylcholinesterase activity in striatum of rats and impairs retention of an inhibitory avoidance task.
Journal: Metabolic brain disease 20080601
Title: Urinary guanidinoacetate and creatine levels in patients with HPRT deficiency.
Journal: Nucleosides, nucleotides & nucleic acids 20080601
Title: Cardiac manifestations in a child with a novel mutation in creatine transporter gene SLC6A8.
Journal: Neurology 20080429
Title: Guanidino compounds after creatine supplementation in renal failure patients and their relation to inflammatory status.
Journal: Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 20080401
Title: Ammonium alters creatine transport and synthesis in a 3D culture of developing brain cells, resulting in secondary cerebral creatine deficiency.
Journal: The European journal of neuroscience 20080401
Title: AGAT, GAMT and SLC6A8 distribution in the central nervous system, in relation to creatine deficiency syndromes: a review.
Journal: Journal of inherited metabolic disease 20080401
Title: Activation of cerebellar granule cells GABA(A) receptors by guanidinoacetate.
Journal: Neuroscience 20080303
Title: Nutritional status has marginal influence on the metabolism of inorganic arsenic in pregnant Bangladeshi women.
Journal: Environmental health perspectives 20080301
Title: Brain proton magnetic resonance spectroscopy and neuromuscular pathology in a patient with GM1 gangliosidosis.
Journal: Journal of child neurology 20080101
Title: Cardiac structure and function during ageing in energetically compromised Guanidinoacetate N-methyltransferase (GAMT)-knockout mice - a one year longitudinal MRI study.
Journal: Journal of cardiovascular magnetic resonance : official journal of the Society for Cardiovascular Magnetic Resonance 20080101
Title: Chaetognath transcriptome reveals ancestral and unique features among bilaterians.
Journal: Genome biology 20080101
Title: Neurotransmitter alterations in embryonic succinate semialdehyde dehydrogenase (SSADH) deficiency suggest a heightened excitatory state during development.
Journal: BMC developmental biology 20080101
Title: Creatine synthesis: production of guanidinoacetate by the rat and human kidney in vivo.
Journal: American journal of physiology. Renal physiology 20071201
Title: Analysis of time-related metabolic fluctuations induced by ethionine in the rat.
Journal: Journal of proteome research 20071201
Title: Changing the substrate specificity of creatine kinase from creatine to glycocyamine: evidence for a highly evolved active site.
Journal: Biochimica et biophysica acta 20071201
Title: Creatine transporter deficiency: prevalence among patients with mental retardation and pitfalls in metabolite screening.
Journal: Clinical biochemistry 20071101
Title: Acute variations in homocysteine levels are related to creatine changes induced by physical activity.
Journal: Clinical nutrition (Edinburgh, Scotland) 20070801
Title: Successful treatment of a guanidinoacetate methyltransferase deficient patient: findings with relevance to treatment strategy and pathophysiology.
Journal: Molecular genetics and metabolism 20070701
Title: Quantification of creatine and guanidinoacetate using GC-MS and LC-MS/MS for the detection of cerebral creatine deficiency syndromes.
Journal: Current protocols in human genetics 20070701
Title: Guanidinoacetate inhibits glutamate uptake in rat striatum of rats at different ages.
Journal: Neurochemical research 20070601
Title: A prevalent pathogenic GAMT mutation (c.59G>C) in Portugal.
Journal: Molecular genetics and metabolism 20070501
Title: Evidence that the inhibitory effects of guanidinoacetate on the activities of the respiratory chain, Na+,K+-ATPase and creatine kinase can be differentially prevented by taurine and vitamins E and C administration in rat striatum in vivo.
Journal: Biochimica et biophysica acta 20070501
Title: Methylation status in females with rett syndrome.
Journal: Journal of child neurology 20070501
Title: Treatment monitoring of brain creatine deficiency syndromes: a 1H- and 31P-MR spectroscopy study.
Journal: AJNR. American journal of neuroradiology 20070301
Title: [Cerebral creatine transporter deficiency: an infradiagnosed neurometabolic disease].
Journal: Revista de neurologia 20070301
Title: Supervised group Lasso with applications to microarray data analysis.
Journal: BMC bioinformatics 20070101
Title: Reactome: a knowledge base of biologic pathways and processes.
Journal: Genome biology 20070101
Title: A top-down systems biology view of microbiome-mammalian metabolic interactions in a mouse model.
Journal: Molecular systems biology 20070101
Title: A transversal approach to predict gene product networks from ontology-based similarity.
Journal: BMC bioinformatics 20070101
Title: International Society of Sports Nutrition position stand: creatine supplementation and exercise.
Journal: Journal of the International Society of Sports Nutrition 20070101
Title: Expression and function of AGAT, GAMT and CT1 in the mammalian brain.
Journal: Sub-cellular biochemistry 20070101
Title: Cerebral creatine deficiency syndromes: clinical aspects, treatment and pathophysiology.
Journal: Sub-cellular biochemistry 20070101
Title: Pre-symptomatic treatment of creatine biosynthesis defects.
Journal: Sub-cellular biochemistry 20070101
Title: Overexpression of GAMT restores GAMT activity in primary GAMT-deficient fibroblasts.
Journal: Molecular genetics and metabolism 20061201
Title: High cerebral guanidinoacetate and variable creatine concentrations in argininosuccinate synthetase and lyase deficiency: implications for treatment?
Journal: Molecular genetics and metabolism 20061101
Title: Influence of hematocrit and localisation of punch in dried blood spots on levels of amino acids and acylcarnitines measured by tandem mass spectrometry.
Journal: Clinica chimica acta; international journal of clinical chemistry 20061101
Title: Reduced intestinal and renal amino acid transport in PDK1 hypomorphic mice.
Journal: FASEB journal : official publication of the Federation of American Societies for Experimental Biology 20061101
Title: Methods for the diagnosis of creatine deficiency syndromes: a comparative study.
Journal: Journal of neuroscience methods 20060930
Title: Anisoin: a useful pre-chromatographic derivatization fluorogenic reagent for LC analysis of guanidino compounds.
Journal: Journal of pharmaceutical and biomedical analysis 20060911
Title: [Diagnosis and treatment of brain creatine deficiency syndromes].
Journal: Revista de neurologia 20060901
Title: Presymptomatic treatment of neonatal guanidinoacetate methyltransferase deficiency.
Journal: Neurology 20060822
Title: GAMT deficiency: features, treatment, and outcome in an inborn error of creatine synthesis.
Journal: Neurology 20060808
Title: S-adenosylhomocysteine hydrolase deficiency in a 26-year-old man.
Journal: Journal of inherited metabolic disease 20060801
Title: Biochemical validation of a rat model for polycystic kidney disease: comparison of guanidino compound profile with the human condition.
Journal: Kidney international 20060601
Title: Cerebral 1H MR spectroscopy showing elevation of brain guanidinoacetate in argininosuccinate lyase deficiency.
Journal: Molecular genetics and metabolism 20060501
Title: Increased guanidino species in murine and human succinate semialdehyde dehydrogenase (SSADH) deficiency.
Journal: Biochimica et biophysica acta 20060401
Title: Prenatal diagnosis of guanidinoacetate methyltransferase deficiency: increased guanidinoacetate concentrations in amniotic fluid.
Journal: Clinical chemistry 20060401
Title: Quantitative short echo time 1H-MR spectroscopy of untreated pediatric brain tumors: preoperative diagnosis and characterization.
Journal: AJNR. American journal of neuroradiology 20060301
Title: Assay for the simultaneous determination of guanidinoacetic acid, creatinine and creatine in plasma and urine by capillary electrophoresis UV-detection.
Journal: Journal of separation science 20060301
Title: Intrastriatal administration of guanidinoacetate inhibits Na+, K+-ATPase and creatine kinase activities in rat striatum.
Journal: Metabolic brain disease 20060301
Title: Quantitative determination of guanidinoacetate and creatine in dried blood spot by flow injection analysis-electrospray tandem mass spectrometry.
Journal: Clinica chimica acta; international journal of clinical chemistry 20060201
Title: Metabolic phenotyping of nude and normal (Alpk:ApfCD, C57BL10J) mice.
Journal: Journal of proteome research 20060201
Title: Theoretical study of the methyl transfer in guanidinoacetate methyltransferase.
Journal: The journal of physical chemistry. B 20060112
Title: A mutation on exon 6 of guanidinoacetate methyltransferase (GAMT) gene supports a different function for isoform a and b of GAMT enzyme.
Journal: Molecular genetics and metabolism 20060101
Title: Urinary excretion of guanidinoacetic acid in rats with diabetic nephropathy.
Journal: Renal failure 20060101
Title: Monitoring the effects of chronic alcohol consumption and abstinence on brain metabolism: a longitudinal proton magnetic resonance spectroscopy study.
Journal: Biological psychiatry 20051215
Title: Folate, homocysteine, and arsenic metabolism in arsenic-exposed individuals in Bangladesh.
Journal: Environmental health perspectives 20051201
Title: Laboratory diagnosis of defects of creatine biosynthesis and transport.
Journal: Clinica chimica acta; international journal of clinical chemistry 20051101
Title: 1H MR spectroscopy of the brain in Cr transporter defect.
Journal: Molecular genetics and metabolism 20051101
Title: Phosphagen kinase of the giant tubeworm Riftia pachyptila. Cloning and expression of cytoplasmic and mitochondrial isoforms of taurocyamine kinase.
Journal: International journal of biological macromolecules 20051030
Title: 1H chemical shift imaging of the brain in guanidino methyltransferase deficiency, a creatine deficiency syndrome; guanidinoacetate accumulation in the gray matter.
Journal: European radiology 20050901
Title: The mimetics of antiadhesive peptides as the inhibitors of Mycobacterium kansasii phagocytosis.
Journal: Peptides 20050901
Title: Lower force and impaired performance during high-intensity electrical stimulation in skeletal muscle of GAMT-deficient knockout mice.
Journal: American journal of physiology. Cell physiology 20050701
Title: Urinary creatinine and arsenic metabolism.
Journal: Environmental health perspectives 20050701
Title: Origin and properties of cytoplasmic and mitochondrial isoforms of taurocyamine kinase.
Journal: The FEBS journal 20050701
Title: Biochemical and behavioural phenotyping of a mouse model for GAMT deficiency.
Journal: Journal of the neurological sciences 20050415
Title: Kinetic behavior of urea is different from that of other water-soluble compounds: the case of the guanidino compounds.
Journal: Kidney international 20050401
Title: Creatine metabolism in combined methylmalonic aciduria and homocystinuria.
Journal: Annals of neurology 20050401
Title: Combinatorial approaches towards the discovery of new tryptase inhibitors.
Journal: Bioorganic & medicinal chemistry letters 20050315
Title: Guanidinoacetate methyltransferase deficiency identified in adults and a child with mental retardation.
Journal: American journal of medical genetics. Part A 20050301
Title: Isolation, characterization, and cDNA-derived amino acid sequence of glycocyamine kinase from the tropical marine worm Namalycastis sp.
Journal: Comparative biochemistry and physiology. Part B, Biochemistry & molecular biology 20050301
Title: [Creatine deficiency syndromes].
Journal: Revue neurologique 20050301
Title: Two novel mutations in SLC6A8 cause creatine transporter defect and distinctive X-linked mental retardation in two unrelated Dutch families.
Journal: American journal of medical genetics. Part A 20050130
Title: A comprehensive update of the sequence and structure classification of kinases.
Journal: BMC structural biology 20050101
Title: Creatine synthesis and transport during rat embryogenesis: spatiotemporal expression of AGAT, GAMT and CT1.
Journal: BMC developmental biology 20050101
Title: Use of denaturing HPLC to provide efficient detection of mutations causing guanidinoacetate methyltransferase deficiency.
Journal: Molecular genetics and metabolism 20050101
Title: L-arginine increases plasma homocysteine in apoE-/-/iNOS-/- double knockout mice.
Journal: Cellular and molecular biology (Noisy-le-Grand, France) 20041201
Title: Catalytic mechanism of guanidinoacetate methyltransferase: crystal structures of guanidinoacetate methyltransferase ternary complexes.
Journal: Biochemistry 20041116
Title: Isoleucine 69 and valine 325 form a specificity pocket in human muscle creatine kinase.
Journal: Biochemistry 20041102
Title: [Guanidino compounds derivatives (guanidinosuccinic acid, guanidinoacetic acid)].
Journal: Nihon rinsho. Japanese journal of clinical medicine 20041101
Title: Phosphorylated guanidinoacetate partly compensates for the lack of phosphocreatine in skeletal muscle of mice lacking guanidinoacetate methyltransferase.
Journal: The Journal of physiology 20041001
Title: Age related reference values for urine creatine and guanidinoacetic acid concentration in children and adolescents by gas chromatography-mass spectrometry.
Journal: Clinica chimica acta; international journal of clinical chemistry 20041001
Title: Plasma guanidino compounds are altered by oral creatine supplementation in healthy humans.
Journal: Journal of applied physiology (Bethesda, Md. : 1985) 20040901
Title: Role of amino-acid residue 95 in substrate specificity of phosphagen kinases.
Journal: FEBS letters 20040827
Title: Determination of guanidinoacetate and creatine in urine and plasma by liquid chromatography-tandem mass spectrometry.
Journal: Clinical chemistry 20040801
Title: Guanidinoacetate methyltransferase deficiency: differences of creatine uptake in human brain and muscle.
Journal: Molecular genetics and metabolism 20040701
Title: Creatine and guanidinoacetate: diagnostic markers for inborn errors in creatine biosynthesis and transport.
Journal: Molecular genetics and metabolism 20040701
Title: Guanidinoacetate and creatine/creatinine levels in controls and patients with urea cycle defects.
Journal: Molecular genetics and metabolism 20040701
Title: Urinary guanidinoacetic acid excretion as an indicator of gentamicin nephrotoxicity in rats.
Journal: Renal failure 20040701
Title: Alternative splicing produces transcripts coding for alpha and beta chains of a hetero-dimeric phosphagen kinase.
Journal: Gene 20040609
Title: In vitro study of the potential role of guanidines in leukocyte functions related to atherogenesis and infection.
Journal: Kidney international 20040601
Title: Evaluation of the mechanism underlying the inhibitory effect of guanidinoacetate on brain Na+, K+-ATPase activity.
Journal: International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience 20040601
Title: Severely altered guanidino compound levels, disturbed body weight homeostasis and impaired fertility in a mouse model of guanidinoacetate N-methyltransferase (GAMT) deficiency.
Journal: Human molecular genetics 20040501
Title: Characterization of seven novel mutations in seven patients with GAMT deficiency.
Journal: Human mutation 20040501
Title: Biochemical and clinical characteristics of creatine deficiency syndromes.
Journal: Acta biochimica Polonica 20040101
Title: The ergogenic potential of arginine.
Journal: Journal of the International Society of Sports Nutrition 20040101
Title: MR spectroscopy of muscle and brain in guanidinoacetate methyltransferase (GAMT)-deficient mice: validation of an animal model to study creatine deficiency.
Journal: Magnetic resonance in medicine 20031101
Title: Creatine supplementation decreases homocysteine in an animal model of uremia.
Journal: Kidney international 20031001
Title: Inhibition of Na+, K+-ATPase activity in rat striatum by guanidinoacetate.
Journal: International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience 20030601
Title: A peculiar result and a fanciful hypothesis regarding L-arginine.
Journal: Arteriosclerosis, thrombosis, and vascular biology 20030601
Title: The nitrate dihydrate of an aquadicopper(II) complex cation with guanidinoacetic acid and a novel trianionic disubstituted guanidine as ligands at 120 K.
Journal: Acta crystallographica. Section C, Crystal structure communications 20030301
Title: A role for guanidino compounds in the brain.
Journal: Molecular and cellular biochemistry 20030201
Title: Creatine deficiency syndromes.
Journal: Molecular and cellular biochemistry 20030201
Title: Stable isotope dilution method for the determination of guanidinoacetic acid by gas chromatography/mass spectrometry.
Journal: Rapid communications in mass spectrometry : RCM 20030101
Title: Clinical characteristics and diagnostic clues in inborn errors of creatine metabolism.
Journal: Journal of inherited metabolic disease 20030101
Title: X-linked creatine transporter defect: an overview.
Journal: Journal of inherited metabolic disease 20030101
Title: Homocystinuria due to cystathionine beta-synthase deficiency: novel biochemical findings and treatment efficacy.
Journal: Journal of inherited metabolic disease 20030101
Title: Polyamine synthesis in plants. Purification and properties of amidinotransferase from soybean (Glycine max) axes.
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Title: Creatine depletion in a new case with AGAT deficiency: clinical and genetic study in a large pedigree.
Journal: Molecular genetics and metabolism 20021201
Title: The blood-brain barrier creatine transporter is a major pathway for supplying creatine to the brain.
Journal: Journal of cerebral blood flow and metabolism : official journal of the International Society of Cerebral Blood Flow and Metabolism 20021101
Title: Activation of GABA(A) receptors by guanidinoacetate: a novel pathophysiological mechanism.
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Title: Guanidinoacetate and creatine plus creatinine assessment in physiologic fluids: an effective diagnostic tool for the biochemical diagnosis of arginine:glycine amidinotransferase and guanidinoacetate methyltransferase deficiencies.
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Title: Tetrakis(mu-guanidinoacetic acid-kappa 2O:O')bis[(nitrato-kappa O)copper(II)].
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Title: Myocellular creatine and creatine transporter serine phosphorylation after starvation.
Journal: The Journal of surgical research 20020601
Title: Dehydration modifies guanidino compound concentrations in the different zones of the rat kidney.
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Title: A novel gene encoding amidinotransferase in the cylindrospermopsin producing cyanobacterium Aphanizomenon ovalisporum.
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Title: Cloning and expression of a lombricine kinase from an echiuroid worm: insights into structural correlates of substrate specificity.
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Title: Long-term effect of partial nephrectomy on biological parameters, kidney histology, and guanidino compound levels in mice.
Journal: Metabolism: clinical and experimental 20011201
Title: Improving treatment of guanidinoacetate methyltransferase deficiency: reduction of guanidinoacetic acid in body fluids by arginine restriction and ornithine supplementation.
Journal: Molecular genetics and metabolism 20011201
Title: Arginine:glycine amidinotransferase deficiency: the third inborn error of creatine metabolism in humans.
Journal: American journal of human genetics 20011101
Title: Methylation demand and homocysteine metabolism: effects of dietary provision of creatine and guanidinoacetate.
Journal: American journal of physiology. Endocrinology and metabolism 20011101
Title: A serine endopeptidase from cucumber leaves is inhibited by L-arginine, guanidino compounds and divalent cations.
Journal: Phytochemistry 20011101
Title: Influence of 72% injury in one kidney on several organs involved in guanidino compound metabolism: a time course study.
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Title: X-linked creatine-transporter gene (SLC6A8) defect: a new creatine-deficiency syndrome.
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Title: Analysis of guanidinoacetate and creatine by isotope dilution electrospray tandem mass spectrometry.
Journal: Clinica chimica acta; international journal of clinical chemistry 20010601
Title: Automated high-performance liquid chromatographic method for the determination of guanidinoacetic acid in dried blood spots: a tool for early diagnosis of guanidinoacetate methyltransferase deficiency.
Journal: Journal of chromatography. B, Biomedical sciences and applications 20010505
Title: Synthesis and biological activity of analogues of the antidiabetic/antiobesity agent 3-guanidinopropionic acid: discovery of a novel aminoguanidinoacetic acid antidiabetic agent.
Journal: Journal of medicinal chemistry 20010412
Title: Synthesis and biological activity of aminoguanidine and diaminoguanidine analogues of the antidiabetic/antiobesity agent 3-guanidinopropionic acid.
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Title: Dichlorobis(glycocyamine-O)copper(II).
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