Title: Valproic acid utilizes the isoleucine breakdown pathway for its complete β-oxidation.
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Title: Beta-ketothiolase deficiency brought with lethargy: case report.
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Title: A novel mutation in the HSD17B10 gene of a 10-year-old boy with refractory epilepsy, choreoathetosis and learning disability.
Journal: PloS one 20110101
Title: Evidence that 2-methylacetoacetate induces oxidative stress in rat brain.
Journal: Metabolic brain disease 20100901
Title: A novel mutation (c.951C>T) in an exonic splicing enhancer results in exon 10 skipping in the human mitochondrial acetoacetyl-CoA thiolase gene.
Journal: Molecular genetics and metabolism 20100801
Title: Molecular weight and thermal properties of polyhydroxyalkanoates produced from fermented sugar molasses by open mixed cultures.
Journal: Journal of biotechnology 20100601
Title: Production of polyhydroxyalkanoates from fermented sugar cane molasses by a mixed culture enriched in glycogen accumulating organisms.
Journal: Journal of biotechnology 20100201
Title: Glial metabolism of isoleucine.
Journal: Neurochemical research 20090101
Title: Study of patients and carriers with 2-methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency: difficulties in the diagnosis.
Journal: Clinical biochemistry 20090101
Title: [Synthesis of brassinolide and its biosynthetic precursors using methyl-3-hydroxy-2-methylpropionate].
Journal: Bioorganicheskaia khimiia 20090101
Title: Characterisation of polyhydroxyalkanoate copolymers with controllable four-monomer composition.
Journal: Journal of biotechnology 20080320
Title: Metabolic modelling of polyhydroxyalkanoate copolymers production by mixed microbial cultures.
Journal: BMC systems biology 20080101
Title: Rapid microwave assisted esterification method for the analysis of poly-3-hydroxybutyrate in Alcaligenes latus by gas chromatography.
Journal: Journal of chromatography. A 20070622
Title: Enantioselective total synthesis of batzelladine F and definition of its structure.
Journal: Journal of the American Chemical Society 20060301
Title: Inhibition of energy metabolism by 2-methylacetoacetate and 2-methyl-3-hydroxybutyrate in cerebral cortex of developing rats.
Journal: Journal of inherited metabolic disease 20050101
Title: Spastic diplegia and periventricular white matter abnormalities in 2-methyl-3-hydroxybutyryl-CoA dehydrogenase deficiency, a defect of isoleucine metabolism: differential diagnosis with hypoxic-ischemic brain diseases.
Journal: Molecular genetics and metabolism 20040401
Title: 2-Methyl-3-hydroxybutyryl-CoA dehydrogenase deficiency: impaired catabolism of isoleucine presenting as neurodegenerative disease.
Journal: Brain & development 20040101
Title: 3-Hydroxy-2-methylbutyryl-CoA dehydrogenase deficiency.
Journal: Journal of inherited metabolic disease 20030101
Title: The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity.
Journal: Journal of inherited metabolic disease 20030101
Title: Total synthesis of (-)-bafilomycin A(1).
Journal: Journal of the American Chemical Society 20020619
