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Title: Crystallization and preliminary X-ray crystallographic studies of succinic semialdehyde dehydrogenase from Streptococcus pyogenes.
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Title: Ethyl 2-[(2,4-difluoro-phen-yl)hydrazinyl-idene]-3-oxobutano-ate.
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Title: Identification of protein networks involved in the disease course of experimental autoimmune encephalomyelitis, an animal model of multiple sclerosis.
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Title: A novel NADH-dependent and FAD-containing hydroxylase is crucial for nicotine degradation by Pseudomonas putida.
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Title: 4-[(2,4-Difluoro-phen-yl)hydrazinyl-idene]-3-methyl-5-oxo-4,5-dihydro-1H-pyrazole-1-carbothio-amide.
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Title: 4-[2-(4-Chloro-phen-yl)hydrazinyl-idene]-3-methyl-5-oxo-4,5-dihydro-1H-pyrazole-1-carbothio-amide.
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Title: 4-[2-(4-Bromo-phen-yl)hydrazinyl-idene]-3-methyl-5-oxo-4,5-dihydro-1H-pyrazole-1-carbothio-amide.
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Title: Succinic semialdehyde dehydrogenase is involved in the robust patterning of Arabidopsis leaves along the adaxial-abaxial axis.
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Title: Common features and differences in the expression of the three genes forming the UGA regulon in Saccharomyces cerevisiae.
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Title: The Agrobacterium tumefaciens transcription factor BlcR is regulated via oligomerization.
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Title: Familial 6p22.2 duplication associates with mild developmental delay and increased SSADH activity.
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Title: The role of aldehyde reductase AKR1A1 in the metabolism of γ-hydroxybutyrate in 1321N1 human astrocytoma cells.
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Title: Analysis of the Aspergillus fumigatus proteome reveals metabolic changes and the activation of the pseurotin A biosynthesis gene cluster in response to hypoxia.
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Title: On the chemical mechanism of succinic semialdehyde dehydrogenase (GabD1) from Mycobacterium tuberculosis.
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Title: GABA metabolism pathway genes, UGA1 and GAD1, regulate replicative lifespan in Saccharomyces cerevisiae.
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Title: The ATXN1 and TRIM31 genes are related to intelligence in an ADHD background: evidence from a large collaborative study totaling 4,963 subjects.
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Title: 4-Hydroxybutyric aciduria associated with catheter usage: a diagnostic pitfall in the identification of SSADH deficiency.
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Title: The bZIP transcription factor MoAP1 mediates the oxidative stress response and is critical for pathogenicity of the rice blast fungus Magnaporthe oryzae.
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Title: A modified rapid enzymatic microtiter plate assay for the quantification of intracellular γ-aminobutyric acid and succinate semialdehyde in bacterial cells.
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Title: Comparative genome analysis and genome-guided physiological analysis of Roseobacter litoralis.
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Title: Complete genome sequence of Corynebacterium variabile DSM 44702 isolated from the surface of smear-ripened cheeses and insights into cheese ripening and flavor generation.
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Title: Dynamic proteomic profiling of a unicellular cyanobacterium Cyanothece ATCC51142 across light-dark diurnal cycles.
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Title: Aldehyde Dehydrogenases in Arabidopsis thaliana: Biochemical Requirements, Metabolic Pathways, and Functional Analysis.
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Title: Head bobbing due to succinic semialdehyde dehydrogenase deficiency.
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Title: Sleep disorders in succinic semialdehyde dehydrogenase deficiency: a family report.
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Title: Atlas of rice grain filling-related metabolism under high temperature: joint analysis of metabolome and transcriptome demonstrated inhibition of starch accumulation and induction of amino acid accumulation.
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Title: Glycolysis and the tricarboxylic acid cycle are linked by alanine aminotransferase during hypoxia induced by waterlogging of Lotus japonicus.
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Title: Structure determination and characterization of the vitamin B6 degradative enzyme (E)-2-(acetamidomethylene)succinate hydrolase.
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Title: A new case of GABA transaminase deficiency facilitated by proton MR spectroscopy.
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Title: The Arabidopsis pop2-1 mutant reveals the involvement of GABA transaminase in salt stress tolerance.
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Title: Complete genome sequence and lifestyle of black-pigmented Corynebacterium aurimucosum ATCC 700975 (formerly C. nigricans CN-1) isolated from a vaginal swab of a woman with spontaneous abortion.
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Title: The X-ray crystal structure of Escherichia coli succinic semialdehyde dehydrogenase; structural insights into NADP+/enzyme interactions.
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Title: The complete genome sequence of Cupriavidus metallidurans strain CH34, a master survivalist in harsh and anthropogenic environments.
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Title: Development and analysis of an in vivo-compatible metabolic network of Mycobacterium tuberculosis.
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Title: The arthrobacter arilaitensis Re117 genome sequence reveals its genetic adaptation to the surface of cheese.
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Title: Interaction with diurnal and circadian regulation results in dynamic metabolic and transcriptional changes during cold acclimation in Arabidopsis.
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Title: Targeting the OB-Folds of Replication Protein A with Small Molecules.
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Title: Polysomnographic abnormalities in succinic semialdehyde dehydrogenase (SSADH) deficiency.
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Title: Decreased GABA-A binding on FMZ-PET in succinic semialdehyde dehydrogenase deficiency.
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Title: Ethyl 2-[(2,6-dimethyl-phen-yl)hydrazono]-3-oxobutanoate.
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Title: The characteristics and mechanisms of pyridine biodegradation by Streptomyces sp.
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Title: Metabolite profiling reveals YihU as a novel hydroxybutyrate dehydrogenase for alternative succinic semialdehyde metabolism in Escherichia coli.
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Title: Succinic semialdehyde dehydrogenase deficiency: lessons from mice and men.
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Title: Sensory integration intervention: historical concepts, treatment strategies and clinical experiences in three patients with succinic semialdehyde dehydrogenase (SSADH) deficiency.
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Title: Ethyl 2-[(3-chloro-phen-yl)hydrazono]-3-oxobutanoate.
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Title: Ethyl 2-[(4-chloro-phen-yl)hydrazono]-3-oxobutanoate.
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Title: Redox-switch modulation of human SSADH by dynamic catalytic loop.
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Title: The conserved R166 residue of ALDH5A (succinic semialdehyde dehydrogenase) has multiple functional roles.
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Title: The effects of a ketogenic diet on ATP concentrations and the number of hippocampal mitochondria in Aldh5a1(-/-) mice.
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Title: Detection of an L-amino acid dehydrogenase activity in Synechocystis sp. PCC 6803.
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Title: GrowMatch: an automated method for reconciling in silico/in vivo growth predictions.
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Title: Gamma-hydroxybutyric acid and its relevance in neurology.
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Title: Insight into the molecular requirements for pathogenicity of Fusarium oxysporum f. sp. lycopersici through large-scale insertional mutagenesis.
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Title: Comparative genomics of aldehyde dehydrogenase 5a1 (succinate semialdehyde dehydrogenase) and accumulation of gamma-hydroxybutyrate associated with its deficiency.
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Title: An ATP and oxalate generating variant tricarboxylic acid cycle counters aluminum toxicity in Pseudomonas fluorescens.
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Title: Deep RNA sequencing of L. monocytogenes reveals overlapping and extensive stationary phase and sigma B-dependent transcriptomes, including multiple highly transcribed noncoding RNAs.
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Title: Phylogenomics of sterol synthesis: insights into the origin, evolution, and diversity of a key eukaryotic feature.
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Title: SSADH deficiency leads to elevated extracellular GABA levels and increased GABAergic neurotransmission in the mouse cerebral cortex.
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Title: 'Succinic semialdehyde dehydrogenase deficiency: phenotype evolution in an adolescent patient at 20-year follow-up'.
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Title: Succinic semialdehyde dehydrogenase from the parasitic cattle tick Rhipicephalus microplus: gene identification, biochemical characterization and comparison with the mouse ortholog.
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Title: Inherited metabolic diseases in neurodevelopmental and neurobehavioral disorders.
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Title: Saturation transfer difference NMR studies on substrates and inhibitors of succinic semialdehyde dehydrogenases.
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Title: Circadian distribution of generalized tonic-clonic seizures associated with murine succinic semialdehyde dehydrogenase deficiency, a disorder of GABA metabolism.
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Title: Neuropsychiatric morbidity in adolescent and adult succinic semialdehyde dehydrogenase deficiency patients.
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Title: Molecular cloning, partial genomic structure and functional characterization of succinic semialdehyde dehydrogenase genes from the parasitic insects Lucilia cuprina and Ctenocephalides felis.
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Title: Identification and characterization of a plastid-localized Arabidopsis glyoxylate reductase isoform: comparison with a cytosolic isoform and implications for cellular redox homeostasis and aldehyde detoxification.
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Title: Gamma-hydroxybutyrate accumulation in Arabidopsis and tobacco plants is a general response to abiotic stress: putative regulation by redox balance and glyoxylate reductase isoforms.
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Title: Gene identification and characterization of the pyridoxine degradative enzyme alpha-(N-acetylaminomethylene)succinic acid amidohydrolase from Mesorhizobium loti MAFF303099.
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Title: Trans-4-hydroxy-2-hexenal is a neurotoxic product of docosahexaenoic (22:6; n-3) acid oxidation.
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Title: Ketogenic diet: stoking energy stores and still posing questions.
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Title: Physiological and molecular adaptations to drought in Andean potato genotypes.
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Title: Options for biochemical production of 4-hydroxybutyrate and its lactone as a substitute for petrochemical production.
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Title: A ketogenic diet rescues the murine succinic semialdehyde dehydrogenase deficient phenotype.
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Title: Functional characterization of a Drosophila melanogaster succinic semialdehyde dehydrogenase and a non-specific aldehyde dehydrogenase.
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Title: Inhibitory effect of Erigeron breviscapus extract and its flavonoid components on GABA shunt enzymes.
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Title: Quantitative 1H NMR metabolomics reveals extensive metabolic reprogramming of primary and secondary metabolism in elicitor-treated opium poppy cell cultures.
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Title: Rapid acid treatment of Escherichia coli: transcriptomic response and recovery.
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Title: Metabolic pathways of the wheat (Triticum aestivum) endosperm amyloplast revealed by proteomics.
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Title: The plant Apolipoprotein D ortholog protects Arabidopsis against oxidative stress.
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Title: Mutants of GABA transaminase (POP2) suppress the severe phenotype of succinic semialdehyde dehydrogenase (ssadh) mutants in Arabidopsis.
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Title: Neurotransmitter alterations in embryonic succinate semialdehyde dehydrogenase (SSADH) deficiency suggest a heightened excitatory state during development.
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Title: Global transcriptional responses of Pseudomonas syringae DC3000 to changes in iron bioavailability in vitro.
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Title: Altered cerebral glucose and acetate metabolism in succinic semialdehyde dehydrogenase-deficient mice: evidence for glial dysfunction and reduced glutamate/glutamine cycling.
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Title: Multicentre search for genetic susceptibility loci in sporadic epilepsy syndrome and seizure types: a case-control study.
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Title: Exploration of intraclonal adaptation mechanisms of Pseudomonas brassicacearum facing cadmium toxicity.
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Title: Diagnostic challenges in a severely delayed infant with hypersomnolence, failure to thrive and arteriopathy: a unique case of gamma-hydroxybutyric aciduria and Williams syndrome.
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Title: Evidence for oxidative stress in tissues derived from succinate semialdehyde dehydrogenase-deficient mice.
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Title: Identification of a novel glyoxylate reductase supports phylogeny-based enzymatic substrate specificity prediction.
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Title: Pseudomonas putida 06909 genes expressed during colonization on mycelial surfaces and phenotypic characterization of mutants.
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Title: Therapeutic concepts in succinate semialdehyde dehydrogenase (SSADH; ALDH5a1) deficiency (gamma-hydroxybutyric aciduria). Hypotheses evolved from 25 years of patient evaluation, studies in Aldh5a1-/- mice and characterization of gamma-hydroxybutyric acid pharmacology.
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Title: Enantioselective oxidation of trans-4-hydroxy-2-nonenal is aldehyde dehydrogenase isozyme and Mg2+ dependent.
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Title: Lipid abnormalities in succinate semialdehyde dehydrogenase (Aldh5a1-/-) deficient mouse brain provide additional evidence for myelin alterations.
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Title: Vigabatrin improves paroxysmal dystonia in succinic semialdehyde dehydrogenase deficiency.
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Title: Enzymatic and metabolic evidence for a region specific mitochondrial dysfunction in brains of murine succinic semialdehyde dehydrogenase deficiency (Aldh5a1-/- mice).
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Title: Inhibition of aldehyde detoxification in CNS mitochondria by fungicides.
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Title: Crystal structures of an Extracytoplasmic Solute Receptor from a TRAP transporter in its open and closed forms reveal a helix-swapped dimer requiring a cation for alpha-keto acid binding.
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Title: The crystal structure of Escherichia coli TdcF, a member of the highly conserved YjgF/YER057c/UK114 family.
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Title: [Role of transamination in the mobilization of respiratory substrates in germinating seeds of castor oil plants].
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Title: Comparative genomics of Bordetella pertussis reveals progressive gene loss in Finnish strains.
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Title: Exploring the functional role of the CHRM2 gene in human cognition: results from a dense genotyping and brain expression study.
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Title: Bioinformatic evaluation of L-arginine catabolic pathways in 24 cyanobacteria and transcriptional analysis of genes encoding enzymes of L-arginine catabolism in the cyanobacterium Synechocystis sp. PCC 6803.
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Title: Oxo-4-methylpentanoic acid directs the metabolism of GABA into the Krebs cycle in rat pancreatic islets.
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Title: Global analysis of gene expression during development and ripening of citrus fruit flesh. A proposed mechanism for citric Acid utilization.
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Title: Succinic semialdehyde couples stress response to quorum-sensing signal decay in Agrobacterium tumefaciens.
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Title: Rhodococcus sp. strain TM1 plays a synergistic role in the degradation of piperidine by Mycobacterium sp. strain THO100.
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Title: Succinic semialdehyde dehydrogenase (SSADH) deficiency: Molecular analysis in a South American family.
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Title: Clinical, cytogenetic and molecular characterization of a patient with combined succinic semialdehyde dehydrogenase deficiency and incomplete WAGR syndrome with obesity.
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Title: SSADH variation in primates: intra- and interspecific data on a gene with a potential role in human cognitive functions.
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Title: Succinic semialdehyde dehydrogenase deficiency: GABAB receptor-mediated function.
Journal: Brain research 20060523
Title: Succinate semialdehyde dehydrogenase deficiency does not down-regulate gamma-hydroxybutyric acid binding sites in the mouse brain.
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Title: D-2-hydroxyglutaric aciduria in three patients with proven SSADH deficiency: genetic coincidence or a related biochemical epiphenomenon?
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Title: Candidate gene analysis of the succinic semialdehyde dehydrogenase gene (ALDH5A1) in patients with idiopathic generalized epilepsy and photosensitivity.
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Title: Increased guanidino species in murine and human succinate semialdehyde dehydrogenase (SSADH) deficiency.
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Title: Final steps in the catabolism of nicotine.
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Title: Metabolism of gamma-hydroxybutyrate to d-2-hydroxyglutarate in mammals: further evidence for d-2-hydroxyglutarate transhydrogenase.
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Title: Succinic semialdehyde dehydrogenase deficiency: clinical, biochemical and molecular characterization of a new patient with severe phenotype and a novel mutation.
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Title: Inhibition of GABA shunt enzymes' activity by 4-hydroxybenzaldehyde derivatives.
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Title: Expression profiling reveals multiple myelin alterations in murine succinate semialdehyde dehydrogenase deficiency.
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Title: Status epilepticus in mice deficient for succinate semialdehyde dehydrogenase: GABAA receptor-mediated mechanisms.
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Title: Predicting genes for orphan metabolic activities using phylogenetic profiles.
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Title: The genome of Rhizobium leguminosarum has recognizable core and accessory components.
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Title: A human derived SSADH coding variant is replacing the ancestral allele shared with primates.
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Title: High-level expression and characterization of the recombinant enzyme, and tissue distribution of human succinic semialdehyde dehydrogenase.
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Title: [Construction of recombinant Escherichia coli strains producing poly (4-hydroxybutyric acid) homopolyester from glucose].
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Title: Effect of genetically caused excess of brain gamma-hydroxybutyric acid and GABA on sleep.
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Title: GABA shunt deficiencies and accumulation of reactive oxygen intermediates: insight from Arabidopsis mutants.
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Title: Gamma-hydroxybutyric aciduria: a biochemist's education from a heritable disorder of GABA metabolism.
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Title: [The role of succinate dehydrogenase in bacterial resistance to the delta endotoxins of Bacillus thuringiensis].
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Title: Emerging experimental therapeutics for bipolar disorder: insights from the molecular and cellular actions of current mood stabilizers.
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Title: Seizure evolution and amino acid imbalances in murine succinate semialdehyde dehydrogenase (SSADH) deficiency.
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Title: Neurodevelopmental pattern of succinic semialdehyde dehydrogenase deficiency (gamma-hydroxybutyric aciduria).
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Title: The ALDH gene superfamily of Arabidopsis.
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Title: A functional polymorphism in the succinate-semialdehyde dehydrogenase (aldehyde dehydrogenase 5 family, member A1) gene is associated with cognitive ability.
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Title: Monitoring gamma-hydroxybutyric acid levels in succinate-semialdehyde dehydrogenase deficiency.
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Title: Liver-directed adenoviral gene transfer in murine succinate semialdehyde dehydrogenase deficiency.
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Title: GABA in plants: just a metabolite?
Journal: Trends in plant science 20040301
Title: Reliable, sensitive, rapid and quantitative enzyme-based assay for gamma-hydroxybutyric acid (GHB).
Journal: Journal of forensic sciences 20040301
Title: 8-cyclopentadienyltricarbonyl 99mtc 8-oxooctanoic acid: a novel radiotracer for evaluation of medium chain fatty acid metabolism in the liver.
Journal: Bioconjugate chemistry 20040101
Title: Sedation with 4-hydroxybutyric acid: a potential pitfall in the diagnosis of SSADH deficiency.
Journal: Journal of inherited metabolic disease 20040101
Title: Succinic semialdehyde dehydrogenase deficiency (SSADH) (4-hydroxybutyric aciduria, gamma-hydroxybutyric aciduria).
Journal: European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 20040101
Title: Mutational spectrum of the succinate semialdehyde dehydrogenase (ALDH5A1) gene and functional analysis of 27 novel disease-causing mutations in patients with SSADH deficiency.
Journal: Human mutation 20031201
Title: Steady-state kinetics and molecular evolution of Escherichia coli MenD [(1R,6R)-2-succinyl-6-hydroxy-2,4-cyclohexadiene-1-carboxylate synthase], an anomalous thiamin diphosphate-dependent decarboxylase-carboligase.
Journal: Biochemistry 20031125
Title: Monitoring of 4-hydroxybutyric acid levels in body fluids during vigabatrin treatment in succinic semialdehyde dehydrogenase deficiency.
Journal: Annals of neurology 20031101
Title: A novel gamma-hydroxybutyrate dehydrogenase: identification and expression of an Arabidopsis cDNA and potential role under oxygen deficiency.
Journal: The Journal of biological chemistry 20031017
Title: Significant behavioral disturbances in succinic semialdehyde dehydrogenase (SSADH) deficiency (gamma-hydroxybutyric aciduria).
Journal: Biological psychiatry 20031001
Title: [A case of succinic semialdehyde dehydrogenase deficiency].
Journal: Zhonghua er ke za zhi = Chinese journal of pediatrics 20030901
Title: Effect of valproic acid on the urinary metabolic profile of a patient with succinic semialdehyde dehydrogenase deficiency.
Journal: Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20030715
Title: Oxidation of 4-hydroxy-2-nonenal by succinic semialdehyde dehydrogenase (ALDH5A).
Journal: Journal of neurochemistry 20030701
Title: Clinical spectrum of succinic semialdehyde dehydrogenase deficiency.
Journal: Neurology 20030513
Title: Cloning and characterization of a gene cluster involved in tetrahydrofuran degradation in Pseudonocardia sp. strain K1.
Journal: Archives of microbiology 20030401
Title: The altered expression of GABA shunt enzymes in the gerbil hippocampus before and after seizure generation.
Journal: Neurochemistry international 20030201
Title: Substrate specificity of mouse aldo-keto reductase AKR7A5.
Journal: Chemico-biological interactions 20030201
Title: A relational database for the discovery of genes encoding amino acid biosynthetic enzymes in pathogenic fungi.
Journal: Comparative and functional genomics 20030201
Title: Inhibition of succinic semialdehyde dehydrogenase activity by alkenal products of lipid peroxidation.
Journal: Biochimica et biophysica acta 20030120
Title: Dietary protein restriction causes modification in aluminum-induced alteration in glutamate and GABA system of rat brain.
Journal: BMC neuroscience 20030101
Title: GABA, gamma-hydroxybutyric acid, and neurological disease.
Journal: Annals of neurology 20030101
Title: Vigabatrin and newer interventions in succinic semialdehyde dehydrogenase deficiency.
Journal: Annals of neurology 20030101
Title: Succinic semialdehyde dehydrogenase deficiency in children and adults.
Journal: Annals of neurology 20030101
Title: Murine succinate semialdehyde dehydrogenase deficiency.
Journal: Annals of neurology 20030101
Title: [Dynamics of local oxygen consumption an extraction under the condition of altered oxygen turnover in humans during head-down bed rest].
Journal: Aviakosmicheskaia i ekologicheskaia meditsina = Aerospace and environmental medicine 20030101
Title: Phytol, SSADH inhibitory diterpenoid of Lactuca sativa.
Journal: Archives of pharmacal research 20021001
Title: Prenatal diagnosis of succinate semialdehyde dehydrogenase deficiency in non-identical twins.
Journal: Journal of inherited metabolic disease 20021001
Title: Novel homodimeric and heterodimeric rat gamma-hydroxybutyrate synthases that associate with the Golgi apparatus define a distinct subclass of aldo-keto reductase 7 family proteins.
Journal: The Biochemical journal 20020915
Title: Rapid and sensitive detection of urinary 4-hydroxybutyric acid and its related compounds by gas chromatography-mass spectrometry in a patient with succinic semialdehyde dehydrogenase deficiency.
Journal: Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20020825
Title: Selective involvement of the globus pallidus and dentate nucleus in succinic semialdehyde dehydrogenase deficiency.
Journal: Pediatric radiology 20020801
Title: Structure of human succinic semialdehyde dehydrogenase gene: identification of promoter region and alternatively processed isoforms.
Journal: Molecular genetics and metabolism 20020801
Title: Spatial and temporal alterations in the GABA shunt in the gerbil hippocampus following transient ischemia.
Journal: Brain research 20020719
Title: Characterisation of a novel mouse liver aldo-keto reductase AKR7A5.
Journal: FEBS letters 20020717
Title: Therapeutic intervention in mice deficient for succinate semialdehyde dehydrogenase (gamma-hydroxybutyric aciduria).
Journal: The Journal of pharmacology and experimental therapeutics 20020701
Title: GabR, a member of a novel protein family, regulates the utilization of gamma-aminobutyrate in Bacillus subtilis.
Journal: Molecular microbiology 20020701
Title: Purification and characterization of aminobutyraldehyde dehydrogenase from Arthrobacter Sp. TMP-1.
Journal: Journal of biochemistry, molecular biology, and biophysics : JBMBB : the official journal of the Federation of Asian and Oceanian Biochemists and Molecular Biologists (FAOBMB) 20020601
Title: Focal neurometabolic alterations in mice deficient for succinate semialdehyde dehydrogenase.
Journal: Journal of neurochemistry 20020401
Title: Production of gamma-hydroxybutyric acid in postmortem liver increases with time after death.
Journal: Toxicology letters 20020328
Title: Neuroleptic malignant syndrome in a patient with succinic semialdehyde dehydrogenase deficiency.
Journal: Pharmacopsychiatry 20020101
Title: Evidence that gamma-aminobutyric acid is a major nitrogen source during Cladosporium fulvum infection of tomato.
Journal: Planta 20020101
Title: Mutation analysis in a patient with succinic semialdehyde dehydrogenase deficiency: a compound heterozygote with 103-121del and 1460T > A of the ALDH5A1 gene.
Journal: Human heredity 20020101
Title: A unique mouse model for succinic semialdehyde dehydrogenase deficiency with implications for gamma hydroxybutyrate intoxication.
Journal: The pharmacogenomics journal 20020101
Title: [Changes in the level of short-chain volatile fatty acids and their aldehydes in oral air and fluid during inflammation of oral tissues].
Journal: Patologicheskaia fiziologiia i eksperimental'naia terapiia 20020101
Title: Pharmacologic rescue of lethal seizures in mice deficient in succinate semialdehyde dehydrogenase.
Journal: Nature genetics 20011001
Title: Prenatal diagnosis of succinic semialdehyde dehydrogenase deficiency: increased accuracy employing DNA, enzyme, and metabolite analyses.
Journal: Molecular genetics and metabolism 20010301
Title: The first case of 4-hydroxybutyric aciduria in Japan.
Journal: Brain & development 20010301
Title: Brain succinic semialdehyde dehydrogenase: identification of reactive lysyl residues labeled with pyridoxal-5'-phosphate.
Journal: Journal of neurochemistry 20010201
Title: Expression of a glutamate decarboxylase homologue is required for normal oxidative stress tolerance in Saccharomyces cerevisiae.
Journal: The Journal of biological chemistry 20010105
Title: Major differences exist in the function and tissue-specific expression of human aflatoxin B1 aldehyde reductase and the principal human aldo-keto reductase AKR1 family members.
Journal: The Biochemical journal 19991015
