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Title: Mutations in BCKD-kinase lead to a potentially treatable form of autism with epilepsy.
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Title: Engineering a metabolic pathway for isobutanol biosynthesis in Bacillus subtilis.
Journal: Applied biochemistry and biotechnology 20120901
Title: Tissue-specific and nutrient regulation of the branched-chain α-keto acid dehydrogenase phosphatase, protein phosphatase 2Cm (PP2Cm).
Journal: The Journal of biological chemistry 20120706
Title: A novel ion-pair RP-HPLC method for determination of five components in compound α-ketoacid tablets.
Journal: Journal of pharmaceutical and biomedical analysis 20120701
Title: Prospective study of changes in the metabolomic profiles of men during their first three months of androgen deprivation therapy for prostate cancer.
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Title: Selective editing of Val and Leu methyl groups in high molecular weight protein NMR.
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Title: Experimental evolution of Legionella pneumophila in mouse macrophages leads to strains with altered determinants of environmental survival.
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Title: Two novel mutations in the BCKDHB gene (R170H, Q346R) cause the classic form of maple syrup urine disease (MSUD).
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Title: Production of volatile compounds by Lactobacillus sakei from branched chain α-keto acids.
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Title: Removal of the C-terminal regulatory domain of α-isopropylmalate synthase disrupts functional substrate binding.
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Title: Mutation of zebrafish dihydrolipoamide branched-chain transacylase E2 results in motor dysfunction and models maple syrup urine disease.
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Title: [Acute encephalopathy due to late-onset maple syrup urine disease in a school boy].
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Title: Fermentative production of isobutene.
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Title: A bio-catalytic approach to aliphatic ketones.
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Title: UniDrug-target: a computational tool to identify unique drug targets in pathogenic bacteria.
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Title: Complete Genome of Ignavibacterium album, a Metabolically Versatile, Flagellated, Facultative Anaerobe from the Phylum Chlorobi.
Journal: Frontiers in microbiology 20120101
Title: Recent progress in synthetic biology for microbial production of C3-C10 alcohols.
Journal: Frontiers in microbiology 20120101
Title: Cloning and characterization of a novel 2-ketoisovalerate reductase from the beauvericin producer Fusarium proliferatum LF061.
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Title: Amino acid metabolism in the human fetus at term: leucine, valine, and methionine kinetics.
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Title: Activation of α-keto acid-dependent dioxygenases: application of an {FeNO}7/{FeO2}8 methodology for characterizing the initial steps of O2 activation.
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Title: Emerging perspectives on essential amino acid metabolism in obesity and the insulin-resistant state.
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Title: Use of the valine biosynthetic pathway to convert glucose into isobutanol.
Journal: Journal of industrial microbiology & biotechnology 20110901
Title: Multimodal dynamic response of the Buchnera aphidicola pLeu plasmid to variations in leucine demand of its host, the pea aphid Acyrthosiphon pisum.
Journal: Molecular microbiology 20110901
Title: The organellar genome and metabolic potential of the hydrogen-producing mitochondrion of Nyctotherus ovalis.
Journal: Molecular biology and evolution 20110801
Title: Engineering Bacillus subtilis for isobutanol production by heterologous Ehrlich pathway construction and the biosynthetic 2-ketoisovalerate precursor pathway overexpression.
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Title: Characterization of organic anion-transporting polypeptide (Oatp) 1a1 and 1a4 null mice reveals altered transport function and urinary metabolomic profiles.
Journal: Toxicological sciences : an official journal of the Society of Toxicology 20110801
Title: ¹³C metabolic flux analysis identifies an unusual route for pyruvate dissimilation in mycobacteria which requires isocitrate lyase and carbon dioxide fixation.
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Title: High-flux isobutanol production using engineered Escherichia coli: a bioreactor study with in situ product removal.
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Title: In vivo neuroprotective effect of L-carnitine against oxidative stress in maple syrup urine disease.
Journal: Metabolic brain disease 20110301
Title: Phenylbutyrate therapy for maple syrup urine disease.
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Title: Metabonomic investigation of single and multiple strain Trypanosoma brucei brucei infections.
Journal: The American journal of tropical medicine and hygiene 20110105
Title: From amino acid to glucosinolate biosynthesis: protein sequence changes in the evolution of methylthioalkylmalate synthase in Arabidopsis.
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Title: Molecular breeding of advanced microorganisms for biofuel production.
Journal: Journal of biomedicine & biotechnology 20110101
Title: Asp295 stabilizes the active-site loop structure of pyruvate dehydrogenase, facilitating phosphorylation of ser292 by pyruvate dehydrogenase-kinase.
Journal: Enzyme research 20110101
Title: Housekeeping genes essential for pantothenate biosynthesis are plasmid-encoded in Rhizobium etli and Rhizobium leguminosarum.
Journal: BMC microbiology 20110101
Title: The human postsynaptic density shares conserved elements with proteomes of unicellular eukaryotes and prokaryotes.
Journal: Frontiers in neuroscience 20110101
Title: More than 200 genes required for methane formation from H₂ and CO₂ and energy conservation are present in Methanothermobacter marburgensis and Methanothermobacter thermautotrophicus.
Journal: Archaea (Vancouver, B.C.) 20110101
Title: Systems biology of the qa gene cluster in Neurospora crassa.
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Title: Genetics and molecular biology of the electron flow for sulfate respiration in desulfovibrio.
Journal: Frontiers in microbiology 20110101
Title: Increased isobutanol production in Saccharomyces cerevisiae by overexpression of genes in valine metabolism.
Journal: Biotechnology for biofuels 20110101
Title: Comparative analyses imply that the enigmatic Sigma factor 54 is a central controller of the bacterial exterior.
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Title: Three Korean patients with maple syrup urine disease: four novel mutations in the BCKDHA gene.
Journal: Annals of clinical and laboratory science 20110101
Title: Carbon metabolic pathways in phototrophic bacteria and their broader evolutionary implications.
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Title: Chemometric analysis of biofluids from mice experimentally infected with Schistosoma mansoni.
Journal: Parasites & vectors 20110101
Title: Detailed kinetics and regulation of mammalian 2-oxoglutarate dehydrogenase.
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Title: Duodenal and faecal microbiota of celiac children: molecular, phenotype and metabolome characterization.
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Title: The transcriptome of the novel dinoflagellate Oxyrrhis marina (Alveolata: Dinophyceae): response to salinity examined by 454 sequencing.
Journal: BMC genomics 20110101
Title: Proteomic and biochemical analyses reveal the activation of unfolded protein response, ERK-1/2 and ribosomal protein S6 signaling in experimental autoimmune myocarditis rat model.
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Title: Identification of two novel BCKDHA mutations in a Chinese patient with maple syrup urine disease.
Journal: Journal of pediatric endocrinology & metabolism : JPEM 20110101
Title: The fur transcription regulator and fur-regulated genes in Clostridium botulinum A ATCC 3502.
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Title: Impact of prenatal disorders on the metabolic profile of second trimester amniotic fluid: a nuclear magnetic resonance metabonomic study.
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Title: Proteomic and metabolomic analysis of atrial profibrillatory remodelling in congestive heart failure.
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Title: Graph-based analysis of the metabolic exchanges between two co-resident intracellular symbionts, Baumannia cicadellinicola and Sulcia muelleri, with their insect host, Homalodisca coagulata.
Journal: PLoS computational biology 20100901
Title: Metabolic changes reveal the development of schistosomiasis in mice.
Journal: PLoS neglected tropical diseases 20100801
Title: Engineering Corynebacterium glutamicum for isobutanol production.
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Title: Characterization of the branched-chain amino acid aminotransferase enzyme family in tomato.
Journal: Plant physiology 20100701
Title: LAP5 and LAP6 encode anther-specific proteins with similarity to chalcone synthase essential for pollen exine development in Arabidopsis.
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Title: Microbial 1-butanol production: Identification of non-native production routes and in silico engineering interventions.
Journal: Biotechnology journal 20100701
Title: Complete genome sequence of Thermosphaera aggregans type strain (M11TL).
Journal: Standards in genomic sciences 20100630
Title: Incorporation of methyl-protonated valine and leucine residues into deuterated ocean pout type III antifreeze protein: expression, crystallization and preliminary neutron diffraction studies.
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Title: Integrated cytokine and metabolic analysis of pathological responses to parasite exposure in rodents.
Journal: Journal of proteome research 20100507
Title: Mass spectrometry screening reveals widespread diversity in trichome specialized metabolites of tomato chromosomal substitution lines.
Journal: The Plant journal : for cell and molecular biology 20100501
Title: Integration of metabolomics and transcriptomics data to aid biomarker discovery in type 2 diabetes.
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Title: Analysis of branched-chain alpha-keto acid dehydrogenase complex activity in rat tissues using alpha-keto[1-13C]isocaproate as substrate.
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Title: DNA carrier testing and newborn screening for maple syrup urine disease in Old Order Mennonite communities.
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Title: The effects of branched-chain amino acid interactions on growth performance, blood metabolites, enzyme kinetics and transcriptomics in weaned pigs.
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Title: Structural insights into the prereaction state of pyruvate decarboxylase from Zymomonas mobilis .
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Title: Homeostatic interplay between bacterial cell-cell signaling and iron in virulence.
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Title: The C-terminal regulatory domain is required for catalysis by Neisseria meningitidis alpha-isopropylmalate synthase.
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Title: Regulation of branched-chain amino acid catabolism: glucose limitation enhances the component of isovalerylspiramycin for the bitespiramycin production.
Journal: Bioprocess and biosystems engineering 20100201
Title: Genome sequence of the pea aphid Acyrthosiphon pisum.
Journal: PLoS biology 20100201
Title: Engineering the isobutanol biosynthetic pathway in Escherichia coli by comparison of three aldehyde reductase/alcohol dehydrogenase genes.
Journal: Applied microbiology and biotechnology 20100101
Title: Pentanol isomer synthesis in engineered microorganisms.
Journal: Applied microbiology and biotechnology 20100101
Title: The path to next generation biofuels: successes and challenges in the era of synthetic biology.
Journal: Microbial cell factories 20100101
Title: The Thiamine diphosphate dependent Enzyme Engineering Database: a tool for the systematic analysis of sequence and structure relations.
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Title: Prediction of novel synthetic pathways for the production of desired chemicals.
Journal: BMC systems biology 20100101
Title: alpha-hydroxybutyrate is an early biomarker of insulin resistance and glucose intolerance in a nondiabetic population.
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Title: Compartmentalization of the Edinburgh Human Metabolic Network.
Journal: BMC bioinformatics 20100101
Title: Two origins for the gene encoding alpha-isopropylmalate synthase in fungi.
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Title: Synthetic biology guides biofuel production.
Journal: Journal of biomedicine & biotechnology 20100101
Title: Iron-sulfur world in aerobic and hyperthermoacidophilic archaea Sulfolobus.
Journal: Archaea (Vancouver, B.C.) 20100101
Title: A genomic perspective on the potential of Actinobacillus succinogenes for industrial succinate production.
Journal: BMC genomics 20100101
Title: Interaction with diurnal and circadian regulation results in dynamic metabolic and transcriptional changes during cold acclimation in Arabidopsis.
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Title: A kinetic platform for in silico modeling of the metabolic dynamics in Escherichia coli.
Journal: Advances and applications in bioinformatics and chemistry : AABC 20100101
Title: Adverse effect of fenofibrate on branched-chain alpha-ketoacid dehydrogenase complex in rat's liver.
Journal: Toxicology 20091221
Title: Decreased enzyme activity and contents of hepatic branched-chain alpha-keto acid dehydrogenase complex subunits in a rat model for type 2 diabetes mellitus.
Journal: Metabolism: clinical and experimental 20091001
Title: Arabidopsis thaliana encodes a bacterial-type heterodimeric isopropylmalate isomerase involved in both Leu biosynthesis and the Met chain elongation pathway of glucosinolate formation.
Journal: Plant molecular biology 20091001
Title: Maple syrup urine disease in Cypriot families: identification of three novel mutations and biochemical characterization of the p.Thr211Met mutation in the E1alpha subunit.
Journal: Genetic testing and molecular biomarkers 20091001
Title: Identification of candidate genes affecting Delta9-tetrahydrocannabinol biosynthesis in Cannabis sativa.
Journal: Journal of experimental botany 20090901
Title: Hepatocyte transplantation improves phenotype and extends survival in a murine model of intermediate maple syrup urine disease.
Journal: Molecular therapy : the journal of the American Society of Gene Therapy 20090701
Title: Protein phosphatase 2Cm is a critical regulator of branched-chain amino acid catabolism in mice and cultured cells.
Journal: The Journal of clinical investigation 20090601
Title: Inhibition of branched-chain alpha-ketoacid dehydrogenase kinase by thiamine pyrophosphate at different potassium ionic levels.
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Title: Revisiting MSUD in Portuguese Gypsies: evidence for a founder mutation and for a mutational hotspot within the BCKDHA gene.
Journal: Annals of human genetics 20090501
Title: Animal models of maple syrup urine disease.
Journal: Journal of inherited metabolic disease 20090401
Title: Selective backbone labelling of ILV methyl labelled proteins.
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Title: Modified method for purifying rat liver branched-chain alpha-ketoacid dehydrogenase complex.
Journal: Bioscience, biotechnology, and biochemistry 20090323
Title: The standardized ileal digestible valine-to-lysine requirement ratio is at least seventy percent in postweaned piglets.
Journal: Journal of animal science 20090301
Title: An efficient protocol for the complete incorporation of methyl-protonated alanine in perdeuterated protein.
Journal: Journal of biomolecular NMR 20090201
Title: Combinatorial mutasynthesis of scrambled beauvericins, cyclooligomer depsipeptide cell migration inhibitors from Beauveria bassiana.
Journal: Chembiochem : a European journal of chemical biology 20090126
Title: Identification of additional players in the alternative biosynthesis pathway to isovaleryl-CoA in the myxobacterium Myxococcus xanthus.
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Title: Regulation of alpha-ketoisovalerate decarboxylase expression in Lactococcus lactis IFPL730.
Journal: Journal of molecular microbiology and biotechnology 20090101
Title: Modeling metabolic networks in C. glutamicum: a comparison of rate laws in combination with various parameter optimization strategies.
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Title: Isolation, sequence identification, and tissue expression profile of 3 novel porcine genes: NCF2, BCKDHB and BCKDHA.
Journal: Journal of applied genetics 20090101
Title: Determination of branched chain amino acids, methionine, phenylalanine, tyrosine and alpha-keto acids in plasma and dried blood samples using HPLC with fluorescence detection.
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Title: Molecular genetics of maple syrup urine disease in the Turkish population.
Journal: The Turkish journal of pediatrics 20090101
Title: Characterization of alpha-isopropylmalate synthases containing different copy numbers of tandem repeats in Mycobacterium tuberculosis.
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Title: Molecular cloning, sequence identification and tissue expression profile of three novel sheep (Ovis aries) genes - BCKDHA, NAGA and HEXA.
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Title: The amidase domain of lipoamidase specifically inactivates lipoylated proteins in vivo.
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Title: Snapshots of catalysis in the E1 subunit of the pyruvate dehydrogenase multienzyme complex.
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Title: Protein side-chain dynamics as observed by solution- and solid-state NMR spectroscopy: a similarity revealed.
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Title: Impaired oxidation of branched-chain amino acids in the medial thalamus of thiamine-deficient rats.
Journal: Metabolic brain disease 20081201
Title: Maple syrup urine disease due to a new large deletion at BCKDHA caused by non-homologous recombination.
Journal: Journal of inherited metabolic disease 20081201
Title: Exploration of the molecular origin of the azinomycin epoxide: timing of the biosynthesis revealed.
Journal: Organic letters 20081106
Title: alpha-Isopropylmalate, a leucine biosynthesis intermediate in yeast, is transported by the mitochondrial oxalacetate carrier.
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Title: Direct methods and residue type specific isotope labeling in NMR structure determination and model-driven sequential assignment.
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Title: Maple syrup urine disease in Thai infants.
Journal: Journal of the Medical Association of Thailand = Chotmaihet thangphaet 20081001
Title: Regulation of branched-chain amino acid catabolism in rat models for spontaneous type 2 diabetes mellitus.
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Title: Metabolic profiling of an Echinostoma caproni infection in the mouse for biomarker discovery.
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Title: Structural bases for the specific interactions between the E2 and E3 components of the Thermus thermophilus 2-oxo acid dehydrogenase complexes.
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Title: Molecular and structural analyses of maple syrup urine disease and identification of a founder mutation in a Portuguese Gypsy community.
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Title: A novel isoform of pantothenate synthetase in the Archaea.
Journal: The FEBS journal 20080601
Title: Structure-function relationships in the 2-oxo acid dehydrogenase family: substrate-specific signatures and functional predictions for the 2-oxoglutarate dehydrogenase-like proteins.
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Title: A new family of D-2-hydroxyacid dehydrogenases that comprises D-mandelate dehydrogenases and 2-ketopantoate reductases.
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Title: Branched chain alpha-keto acid dehydrogenase, E1-beta subunit gene is associated with premature ovarian failure.
Journal: Fertility and sterility 20080301
Title: Amino acids allosterically regulate the thiamine diphosphate-dependent alpha-keto acid decarboxylase from Mycobacterium tuberculosis.
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Title: A genomic analysis of the archaeal system Ignicoccus hospitalis-Nanoarchaeum equitans.
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Title: Is gene activity in plant cells affected by UMTS-irradiation? A whole genome approach.
Journal: Advances and applications in bioinformatics and chemistry : AABC 20080101
Title: Obesity-related elevations in plasma leucine are associated with alterations in enzymes involved in branched-chain amino acid metabolism.
Journal: American journal of physiology. Endocrinology and metabolism 20071201
Title: Structure of the branched-chain keto acid decarboxylase (KdcA) from Lactococcus lactis provides insights into the structural basis for the chemoselective and enantioselective carboligation reaction.
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Title: Description of the mutations in 15 subjects with variant forms of maple syrup urine disease.
Journal: Journal of inherited metabolic disease 20071101
Title: Effect of the branched-chain alpha-keto acids accumulating in maple syrup urine disease on S100B release from glial cells.
Journal: Journal of the neurological sciences 20070915
Title: Exercise training increases branched-chain oxoacid dehydrogenase kinase content in human skeletal muscle.
Journal: American journal of physiology. Regulatory, integrative and comparative physiology 20070901
Title: Peroxisomal metabolism of propionic acid and isobutyric acid in plants.
Journal: The Journal of biological chemistry 20070824
Title: L-glutamine in vitro regulates rat aortic glutamate content and modulates nitric oxide formation and contractility responses.
Journal: American journal of physiology. Cell physiology 20070701
Title: Identification of the bkdAB gene cluster, a plausible source of the starter-unit for virginiamycin M production in Streptomyces virginiae.
Journal: Archives of microbiology 20070601
Title: Biomass in the manufacture of industrial products--the use of proteins and amino acids.
Journal: Applied microbiology and biotechnology 20070601
Title: Inhibition of PI3-kinase signaling by glucocorticoids results in increased branched-chain amino acid degradation in renal epithelial cells.
Journal: American journal of physiology. Cell physiology 20070501
Title: MAM3 catalyzes the formation of all aliphatic glucosinolate chain lengths in Arabidopsis.
Journal: Plant physiology 20070501
Title: The two active sites in human branched-chain alpha-keto acid dehydrogenase operate independently without an obligatory alternating-site mechanism.
Journal: The Journal of biological chemistry 20070420
Title: Transcriptional analysis of L-methionine catabolism in Brevibacterium linens ATCC9175.
Journal: Applied microbiology and biotechnology 20070401
Title: Lowered concentrations of branched-chain amino acids result in impaired growth and neurological problems: insights from a branched-chain alpha-keto acid dehydrogenase complex kinase-deficient mouse model.
Journal: Nutrition reviews 20070401
Title: Synaptic plasma membrane Na(+), K (+)-ATPase activity is significantly reduced by the alpha-keto acids accumulating in maple syrup urine disease in rat cerebral cortex.
Journal: Metabolic brain disease 20070301
Title: Two Arabidopsis genes (IPMS1 and IPMS2) encode isopropylmalate synthase, the branchpoint step in the biosynthesis of leucine.
Journal: Plant physiology 20070201
Title: Branched chain keto-acids exert biphasic effects on alpha-ketoglutarate-stimulated respiration in intact rat liver mitochondria.
Journal: Neurochemical research 20070101
Title: The crystal structure of Escherichia coli TdcF, a member of the highly conserved YjgF/YER057c/UK114 family.
Journal: BMC structural biology 20070101
Title: Metabolic network visualization eliminating node redundance and preserving metabolic pathways.
Journal: BMC systems biology 20070101
Title: A comprehensive analysis of non-sequential alignments between all protein structures.
Journal: BMC structural biology 20070101
Title: Single nucleotide polymorphism detection by polymerase chain reaction-restriction fragment length polymorphism.
Journal: Nature protocols 20070101
Title: A synchronized substrate-gating mechanism revealed by cubic-core structure of the bovine branched-chain alpha-ketoacid dehydrogenase complex.
Journal: The EMBO journal 20061213
Title: Determinants of substrate specificity in KdcA, a thiamin diphosphate-dependent decarboxylase.
Journal: Bioorganic chemistry 20061201
Title: Spectroscopic and electronic structure studies of the role of active site interactions in the decarboxylation reaction of alpha-keto acid-dependent dioxygenases.
Journal: Journal of inorganic biochemistry 20061201
Title: Impaired growth and neurological abnormalities in branched-chain alpha-keto acid dehydrogenase kinase-deficient mice.
Journal: The Biochemical journal 20061115
Title: The case for regulating indispensable amino acid metabolism: the branched-chain alpha-keto acid dehydrogenase kinase-knockout mouse.
Journal: The Biochemical journal 20061115
Title: A relevant in vitro eukaryotic live-cell system for the evaluation of plasmodial protein localization.
Journal: Biochimie 20061001
Title: Structure of the subunit binding domain and dynamics of the di-domain region from the core of human branched chain alpha-ketoacid dehydrogenase complex.
Journal: The Journal of biological chemistry 20060922
Title: Kinetic and chemical mechanism of alpha-isopropylmalate synthase from Mycobacterium tuberculosis.
Journal: Biochemistry 20060725
Title: Clofibrate treatment promotes branched-chain amino acid catabolism and decreases the phosphorylation state of mTOR, eIF4E-BP1, and S6K1 in rat liver.
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Title: Mutational spectrum of maple syrup urine disease in Spain.
Journal: Human mutation 20060701
Title: Metabolic complementarity and genomics of the dual bacterial symbiosis of sharpshooters.
Journal: PLoS biology 20060601
Title: Leucine-induced activation of translational initiation is partly regulated by the branched-chain alpha-keto acid dehydrogenase complex in C2C12 cells.
Journal: Biochemical and biophysical research communications 20060519
Title: Hypobaric hypoxia affects endogenous levels of alpha-keto acids in murine heart ventricles.
Journal: Biochemical and biophysical research communications 20060414
Title: IgA class antibodies to 2-oxo-acid dehydrogenase complex are not predictive markers of histopathological progression in primary biliary cirrhosis.
Journal: Autoimmunity 20060301
Title: A versatile conformational switch regulates reactivity in human branched-chain alpha-ketoacid dehydrogenase.
Journal: Structure (London, England : 1993) 20060201
Title: Creatine and antioxidant treatment prevent the inhibition of creatine kinase activity and the morphological alterations of C6 glioma cells induced by the branched-chain alpha-keto acids accumulating in maple syrup urine disease.
Journal: Cellular and molecular neurobiology 20060201
Title: Production and characterization of murine models of classic and intermediate maple syrup urine disease.
Journal: BMC medical genetics 20060101
Title: Metabolite profiling of Chlamydomonas reinhardtii under nutrient deprivation.
Journal: Plant physiology 20051201
Title: Human microRNA (miR29b) expression controls the amount of branched chain alpha-ketoacid dehydrogenase complex in a cell.
Journal: Human molecular genetics 20051115
Title: Folding of the protein domain hbSBD.
Journal: Biophysical journal 20051101
Title: Plasmodium falciparum possesses organelle-specific alpha-keto acid dehydrogenase complexes and lipoylation pathways.
Journal: Biochemical Society transactions 20051101
Title: Mechanism of the insulin-releasing action of alpha-ketoisocaproate and related alpha-keto acid anions.
Journal: Molecular pharmacology 20051001
Title: Coordinated collagen and muscle protein synthesis in human patella tendon and quadriceps muscle after exercise.
Journal: The Journal of physiology 20050915
Title: Branched-chain alpha-keto acids accumulating in maple syrup urine disease induce reorganization of phosphorylated GFAP in C6-glioma cells.
Journal: Metabolic brain disease 20050901
Title: Studies on thiamine diphosphate-dependent enzymes.
Journal: Biochemical Society transactions 20050801
Title: Slow-onset feedback inhibition: inhibition of Mycobacterium tuberculosis alpha-isopropylmalate synthase by L-leucine.
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Title: alpha-keto acids accumulating in maple syrup urine disease stimulate lipid peroxidation and reduce antioxidant defences in cerebral cortex from young rats.
Journal: Metabolic brain disease 20050601
Title: Biosynthesis of glyoxylate from glycine in Saccharomyces cerevisiae.
Journal: FEMS yeast research 20050501
Title: Activation of hepatic branched-chain alpha-keto acid dehydrogenase complex by tumor necrosis factor-alpha in rats.
Journal: Biochemical and biophysical research communications 20050325
Title: A novel mutation in the dihydrolipoamide dehydrogenase E3 subunit gene (DLD) resulting in an atypical form of alpha-ketoglutarate dehydrogenase deficiency.
Journal: Human mutation 20050301
Title: Precursor and temperature modulation of fatty acid composition and growth of Listeria monocytogenes cold-sensitive mutants with transposon-interrupted branched-chain alpha-keto acid dehydrogenase.
Journal: Microbiology (Reading, England) 20050201
Title: Dissociation of branched-chain alpha-keto acid dehydrogenase kinase (BDK) from branched-chain alpha-keto acid dehydrogenase complex (BCKDC) by BDK inhibitors.
Journal: Journal of nutritional science and vitaminology 20050201
Title: The human malaria parasite Plasmodium falciparum possesses two distinct dihydrolipoamide dehydrogenases.
Journal: Molecular microbiology 20050101
Title: Thermococcus profundus 2-ketoisovalerate ferredoxin oxidoreductase, a key enzyme in the archaeal energy-producing amino acid metabolic pathway.
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Title: A comprehensive update of the sequence and structure classification of kinases.
Journal: BMC structural biology 20050101
Title: The mitochondrial branched-chain aminotransferase (AtBCAT-1) is capable to initiate degradation of leucine, isoleucine and valine in almost all tissues in Arabidopsis thaliana.
Journal: Plant molecular biology 20050101
Title: Modeling Lactococcus lactis using a genome-scale flux model.
Journal: BMC microbiology 20050101
Title: Molecular mechanism for regulation of the human mitochondrial branched-chain alpha-ketoacid dehydrogenase complex by phosphorylation.
Journal: Structure (London, England : 1993) 20041201
Title: Evidence that the branched-chain alpha-keto acids accumulating in maple syrup urine disease induce morphological alterations and death in cultured astrocytes from rat cerebral cortex.
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Title: Tissue-specific translation of murine branched-chain alpha-ketoacid dehydrogenase kinase mRNA is dependent upon an upstream open reading frame in the 5'-untranslated region.
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Title: Biochemical and molecular characterization of alpha-ketoisovalerate decarboxylase, an enzyme involved in the formation of aldehydes from amino acids by Lactococcus lactis.
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Title: Conformational stability and thermodynamic characterization of the lipoic acid bearing domain of human mitochondrial branched chain alpha-ketoacid dehydrogenase.
Journal: Protein science : a publication of the Protein Society 20040901
Title: Cross-talk between thiamin diphosphate binding and phosphorylation loop conformation in human branched-chain alpha-keto acid decarboxylase/dehydrogenase.
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Title: Crystallization and preliminary X-ray analysis of alpha-isopropylmalate synthase from Mycobacterium tuberculosis.
Journal: Acta crystallographica. Section D, Biological crystallography 20040601
Title: Glutamine synthesis in the developing porcine placenta.
Journal: Biology of reproduction 20040501
Title: A proteomic investigation of drug-induced steatosis in rat liver.
Journal: Chemical research in toxicology 20040501
Title: Ligand-induced conformational changes and a reaction intermediate in branched-chain 2-oxo acid dehydrogenase (E1) from Thermus thermophilus HB8, as revealed by X-ray crystallography.
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Title: Diversity of L-leucine catabolism in various microorganisms involved in dairy fermentations, and identification of the rate-controlling step in the formation of the potent flavour component 3-methylbutanal.
Journal: Applied microbiology and biotechnology 20040401
Title: A conditional marker gene allowing both positive and negative selection in plants.
Journal: Nature biotechnology 20040401
Title: Leucine toxicity in a neuronal cell model with inhibited branched chain amino acid catabolism.
Journal: Brain research. Molecular brain research 20040330
Title: Differential regulation of branched-chain alpha-ketoacid dehydrogenase kinase expression by glucocorticoids and acidification in LLC-PK1-GR101 cells.
Journal: American journal of physiology. Renal physiology 20040301
Title: Effects of liver failure on branched-chain alpha-keto acid dehydrogenase complex in rat liver and muscle: comparison between acute and chronic liver failure.
Journal: Journal of hepatology 20040301
Title: [Effects of bkdAB interruption on avermectin biosynthesis].
Journal: Sheng wu gong cheng xue bao = Chinese journal of biotechnology 20040301
Title: Lipoic acid-dependent oxidative catabolism of alpha-keto acids in mitochondria provides evidence for branched-chain amino acid catabolism in Arabidopsis.
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Title: Alpha-keto-beta-methylvaleric acid increases the in vitro phosphorylation of intermediate filaments in cerebral cortex of young rats through the gabaergic system.
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Title: Effects of liver failure on the enzymes in the branched-chain amino acid catabolic pathway.
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